A Case of Atypical Cogan’s Syndrome and Review of Literature
نویسندگان
چکیده
Cogan’s Syndrome (CS) is a disease affecting young adults and consists of episodes of acute interstitial keratitis with vestibuloauditory dysfunction. This syndrome was originally described in 1945 by Cogan as a disorder of the eyes and ears, characterized by nonsyphilitic interstitial keratitis with deafness. Sporadic reports showing the development of vasculitis in patients with eye and ear disease have been published over the last 30 years. When ocular signs, in addition to interstitial keratitis, are present, the syndrome is referred to as atypical Cogan’s Syndrome. Although cases of scleritis and posterior scleritis accompanying interstitial keratitis have been reported in the literature (1, 2), iridocyclitis is extremely rare (3). Presented below is a report of an atypical CS with iridocyclitis, and a review of the literature to familarize doctors with this unusual but treatable disorder.
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